Genetic Disorders and the Fetus. Группа авторов

Genetic Disorders and the Fetus - Группа авторов


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7 7 13 5 3 Ulnar–Mammary syndrome (UMS) TBX3 AD 1 3 3 4 1 1 Usher syndrome, type I (USH1) MYO7A AD 1 3 2 2 1 1 Usher syndrome, type IF (USH1F) PCDH15 AR 2 4 4 6 4 2 Usher syndrome, type IIA (USH2A) USH2A AR 3 4 5 6 2 2 Usher syndrome, type IIC (USH2C) ADGRV1 AR 1 1 1 2 1 1 Usher syndrome, type IIC (USH2C) GPR98 AR 1 1 0 0 0 0 Van der Woude syndrome 1 (VWS1) IRF6 AD 3 3 3 3 3 3 Von Hippel–Lindau syndrome (VHL) VHL AD 19 25 21 30 15 14 Waardenburg syndrome, type 2A (WS2A) MITF AD 2 6 6 6 4 4 Wilson disease ATP7B AR 3 3 3 5 3 2 Wiskott–Aldrich syndrome (WAS) WAS XL 6 15 13 20 9 8 Wolfram syndrome 1 (WFS1) WFS1 AR 1 2 1 1 1 1 Xeroderma pigmentosum, complementation group g (XPG) ERCC5 AR 1 1 0 0 0 0 TOTAL 3463 5869 4683 7443 2644 2332 1.59 56.4%

      Polar body‐based preimplantation genetic testing

      The biopsy of gametes opened an intriguing possibility of preconception diagnosis of inherited diseases, because genetic analysis of biopsied gamete material made it realistic to select gametes containing an unaffected allele for fertilization and subsequent transfer.28 In this way, not only was the selective abortion of an affected fetus avoided but also fertilization involving affected gametes, as an option for couples at risk of conceiving a genetically abnormal fetus.

      Although preconception genetic testing could be achieved by genotyping either oocytes or sperm, the latter approach is still not realistic. Development of methods for culture of primary spermatocytes and spermatogonia followed by genetic analysis of matured spermatides is theoretically possible, but this still remains a subject for future research, such as in the framework of the current attempts at haploidization.29, 30 The technique of sperm duplication has been introduced, which may allow testing of the sperm duplicate. However, errors may arise in the reduplication procedure, making the technique of sperm duplication inapplicable for clinical practice.31, 32


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